Sphingolipid metabolism

hsa00600 25 targets in this pathway

UniProt AC Gene Protein Name Organism Multi-Target Molecules
Q9HCG7 GBA2 Non-lysosomal glucosylceramidase Homo sapiens 78 Detail
Q16739 UGCG Ceramide glucosyltransferase Homo sapiens 74 Detail
Q9NRA0 SPHK2 Sphingosine kinase 2 Homo sapiens 60 Detail
Q9NYA1 SPHK1 Sphingosine kinase 1 Homo sapiens 60 Detail
P04062 GBA1 Lysosomal acid glucosylceramidase Homo sapiens 57 Detail
O95470 SGPL1 Sphingosine-1-phosphate lyase 1 Homo sapiens 50 Detail
P07686 HEXB Beta-hexosaminidase subunit beta Homo sapiens 8 Detail
P16278 GLB1 Beta-galactosidase Homo sapiens 7 Detail
O15270 SPTLC2 Serine palmitoyltransferase 2 Homo sapiens 6 Detail
Q13510 ASAH1 Acid ceramidase Homo sapiens 5 Detail
O15269 SPTLC1 Serine palmitoyltransferase 1 Homo sapiens 4 Detail
Q9UQ49 NEU3 Sialidase-3 Homo sapiens 4 Detail
P06280 GLA Alpha-galactosidase A Homo sapiens 4 Detail
P06865 HEXA Beta-hexosaminidase subunit alpha Homo sapiens 4 Detail
Q8WWR8 NEU4 Sialidase-4 Homo sapiens 3 Detail
Q8NHU3 SGMS2 Phosphatidylcholine:ceramide cholinephosphotransferase 2 Homo sapiens 3 Detail
Q9NUV7 SPTLC3 Serine palmitoyltransferase 3 Homo sapiens 3 Detail
O15121 DEGS1 Sphingolipid delta(4)-desaturase DES1 Homo sapiens 3 Detail
Q86VZ5 SGMS1 Phosphatidylcholine:ceramide cholinephosphotransferase 1 Homo sapiens 2 Detail
Q96G23 CERS2 Ceramide synthase 2 Homo sapiens 1 Detail
Q5QJU3 ACER2 Alkaline ceramidase 2 Homo sapiens 1 Detail
Q9NXE4 SMPD4 Sphingomyelin phosphodiesterase 4 Homo sapiens 1 Detail
P27544 CERS1 Ceramide synthase 1 Homo sapiens 0 Detail
O60906 SMPD2 Sphingomyelin phosphodiesterase 2 Homo sapiens 0 Detail
Q16880 UGT8 2-hydroxyacylsphingosine 1-beta-galactosyltransferase Homo sapiens 0 Detail