Valine, leucine and isoleucine degradation
hsa00280 16 targets in this pathway
| UniProt AC | Gene | Protein Name | Organism | Multi-Target Molecules | |
|---|---|---|---|---|---|
P05091 |
ALDH2 | Aldehyde dehydrogenase, mitochondrial | Homo sapiens | 19 | Detail |
P30837 |
ALDH1B1 | Aldehyde dehydrogenase X, mitochondrial | Homo sapiens | 8 | Detail |
Q99714 |
HSD17B10 | 3-hydroxyacyl-CoA dehydrogenase type-2 | Homo sapiens | 7 | Detail |
Q06278 |
AOX1 | Aldehyde oxidase | Homo sapiens | 7 | Detail |
P24752 |
ACAT1 | Acetyl-CoA acetyltransferase, mitochondrial | Homo sapiens | 7 | Detail |
P54687 |
BCAT1 | Branched-chain-amino-acid aminotransferase, cytosolic | Homo sapiens | 6 | Detail |
O15382 |
BCAT2 | Branched-chain-amino-acid aminotransferase, mitochondrial | Homo sapiens | 6 | Detail |
P40939 |
HADHA | Trifunctional enzyme subunit alpha, mitochondrial | Homo sapiens | 2 | Detail |
P55084 |
HADHB | Trifunctional enzyme subunit beta, mitochondrial | Homo sapiens | 2 | Detail |
P42765 |
ACAA2 | 3-ketoacyl-CoA thiolase, mitochondrial | Homo sapiens | 1 | Detail |
P80404 |
ABAT | 4-aminobutyrate aminotransferase, mitochondrial | Homo sapiens | 1 | Detail |
P30084 |
ECHS1 | Enoyl-CoA hydratase, mitochondrial | Homo sapiens | 1 | Detail |
Q16836 |
HADH | Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial | Homo sapiens | 1 | Detail |
P49419 |
ALDH7A1 | Alpha-aminoadipic semialdehyde dehydrogenase | Homo sapiens | 1 | Detail |
P05165 |
PCCA | Propionyl-CoA carboxylase alpha chain, mitochondrial | Homo sapiens | 1 | Detail |
Q9HCC0 |
MCCC2 | Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial | Homo sapiens | 1 | Detail |